Related Experiment Video
Updated: Mar 7, 2026
07:27
Robotic-assisted Left Pneumonectomy For Vanishing Lung Syndrome
Published on: January 23, 2026
314
Bilateral congenital lobar emphysema: staged management
Lindsey Perea1, Thane Blinman2, Joseph Piccione3
1Department of Surgery, Philadelphia College of Osteopathic Medicine, 4170 City Avenue, Philadelphia, PA, 19131, USA.
Journal of Pediatric Surgery
|February 13, 2017
Summary
Management of bilateral congenital lobar emphysema (CLE) in infants can be guided by a staged, image-guided approach. This review suggests that excising both affected lobes may not always be necessary for positive outcomes.
Area of Science:
- Pediatric Surgery
- Thoracic Surgery
- Pulmonology
Background:
- Bilateral congenital lobar emphysema (CLE) is rare, with limited literature guiding its management.
- This study reviews institutional experience with infants diagnosed with bilateral CLE.
Purpose of the Study:
- To evaluate the effectiveness of a tailored, image-guided surgical approach for bilateral CLE in infants.
- To determine if complete excision of all affected lobes is necessary for favorable outcomes.
Main Methods:
- A case series of infants with bilateral CLE treated between 2014 and 2015.
- Preoperative planning utilized computed tomography angiography (CTA) and bronchoscopy.
- Surgical interventions included unilateral lobectomies and staged procedures.
Main Results:
- Four infants with bilateral CLE (affecting RML and LUL) were treated.
- Tailored surgical approaches based on CTA and bronchoscopy were employed.
- Three patients underwent unilateral lobectomies; one had a staged bilateral lobectomy. All achieved normal growth and room air breathing at >1 year follow-up.
- A unique case of bilateral CLE with pulmonary interstitial glycogenosis (PIG) was identified.
Conclusions:
- A staged, image-guided, and physiology-based operative strategy is supported for bilateral CLE.
- Complete excision of both affected lobes may not be mandatory in the short term.
- CTA is crucial for planning; thoracoscopy has no apparent role.
Related Concept Videos
01:29Chronic Obstructive Pulmonary Disease-V: Management
3.3K
Managing Chronic Obstructive Pulmonary Disease (COPD) involves a multifaceted approach to reduce symptoms, prevent exacerbations, improve overall health status, and slow disease progression. Key strategies include lifestyle modifications, pharmacotherapy, supportive therapies, and, in some cases, surgery. Here is an overview of the primary COPD management strategies:
Smoking Cessation
Smoking Cessation
3.3K
01:30Chronic Obstructive Pulmonary Disease-V: Nursing Management
5.4K
Nursing management of Chronic Obstructive Pulmonary Disease (COPD) is crucial for providing thorough care and support to patients. Nurses play an integral role in this process through detailed assessment, careful planning, targeted interventions, and ongoing evaluation. Here's an overview of the critical steps in nursing management for COPD.
Assessment
Assessment
5.4K
01:26COPD: Management Using Bronchodilators and Corticosteroids
1000
Chronic obstructive pulmonary isease (COPD) involves a group of progressive lung disorders characterized by persistent airflow limitation and chronic respiratory symptoms. Asthma-COPD Overlap Syndrome (ACOS), encompassing features of both asthma and Chronic obstructive pulmonary disease (COPD), is a group of progressive lung disorders that includes chronic bronchitis, emphysema, and refractory (non-reversible) asthma. ACOS leads to complex clinical presentations that combine the inflammatory...
1000
01:20Chronic Obstructive Pulmonary Disease-I: Introduction
4.0K
Chronic Obstructive Pulmonary Disease (COPD) is a long-lasting respiratory condition requiring continuous attention and care. It is a progressive lung disease that leads to breathing challenges due to airflow obstruction. It manifests as persistent respiratory symptoms and restricted airflow resulting from abnormalities in the airways and alveoli, usually due to long-term exposure to harmful particles or gases. COPD mainly consists of two primary conditions: emphysema and chronic bronchitis.
4.0K
01:24Cystic Fibrosis: Management
593
Cystic fibrosis (CF) is an autosomal recessive disorder that predominantly affects individuals of Northern European descent, occurring at a rate of 1 in 3500. It is caused by a genetic mutation in a gene on chromosome 7, most commonly the ΔF508 mutation, that codes for the cystic fibrosis transmembrane conductance regulator (CFTR) protein. This results in thicker mucus secretions and obstruction pathologies in multiple organs, including the lungs and sinuses.
Sinus disease and chronic...
Sinus disease and chronic...
593
01:24Chronic Obstructive Pulmonary Disease
2.8K
COPD is defined as a heterogeneous lung condition marked by persistent respiratory symptoms such as dyspnea, cough, and sputum production, caused by abnormalities in the airways that cause airflow obstruction.
Smoking is a primary risk factor for COPD, with over 80% of patients having a history of it. Patients typically experience progressive dyspnea or labored breathing, frequent coughing, and recurrent pulmonary infections. Many eventually succumb to respiratory failure, characterized by...
Smoking is a primary risk factor for COPD, with over 80% of patients having a history of it. Patients typically experience progressive dyspnea or labored breathing, frequent coughing, and recurrent pulmonary infections. Many eventually succumb to respiratory failure, characterized by...
2.8K