Relapsing polychondritis with meningoencephalitis

Monica Tsai1, Mengjun Hu2, Jamie Zussman3

  • 1Department of Internal Medicine, Cedars-Sinai Medical Center, Los Angeles, California, USA.

Cutis
|February 17, 2017
PubMed

Insights

Relapsing polychondritis (RP) with meningoencephalitis (ME) is rare. Steroid treatment showed positive results in a patient with RP-associated ME, suggesting potential benefits for early diagnosis and further research.

Area of Science:

  • Rheumatology
  • Neurology
  • Autoimmune Diseases

Background:

  • Relapsing polychondritis (RP) is a rare systemic autoimmune disease affecting cartilaginous structures.
  • Meningoencephalitis (ME) is a rare but serious systemic manifestation of RP.
  • RP-associated ME presents diagnostic and therapeutic challenges.

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