Double Chambered Right Ventricle: A Rare Diagnosis

Area of Science:

• Cardiology
• Congenital Heart Disease
• Adult Congenital Heart Disease

Background:

• Double chambered right ventricle (DRCV) is a rare congenital heart anomaly characterized by an anomalous division of the right ventricle into two chambers.
• It is often associated with other cardiac malformations, such as ventricular septal defects, pulmonary stenosis, and aortic stenosis.

Observation:

• A 27-year-old female presented with symptoms of congestive heart failure, including pedal edema, abdominal swelling, and exertional dyspnea.
• Physical examination revealed signs of heart failure. Investigations including chest X-ray, ECG, and echocardiography were performed.

Findings:

• Chest X-ray showed mild cardiomegaly with left pleural effusion.
• ECG indicated right axis deviation with right ventricular hypertrophy.
• Echocardiography confirmed the diagnosis of double chambered right ventricle as an isolated anomaly, without any other congenital heart malformations.

Implications:

• This case highlights the importance of considering isolated double chambered right ventricle in adults presenting with heart failure symptoms.
• The absence of associated defects makes this case unique and provides valuable insights into the spectrum of DRCV presentations.
• Early diagnosis and appropriate management, including surgical consideration, are crucial for favorable outcomes in patients with double chambered right ventricle.