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Intracardiac Thrombus in Behçet's Disease
Hayati Eren1, Lütfi Öcal1, Macit Kalçik1
1Department of Cardiology, Kartal Kosuyolu Heart Training and Research Hospital, Istanbul, Turkey.
Insights
Behçet
Area of Science:
- Rheumatology
- Immunology
- Ophthalmology
Background:
- Behçet's disease (BD) is a chronic inflammatory disorder.
- Characterized by recurrent oral/genital ulcers and uveitis.
- Primarily affects young adults (20-30 years), more common in males.
Observation:
- BD has a global prevalence, concentrated in Mediterranean regions and Japan.
- Multisystemic involvement includes skin, joints, neurological, respiratory, GI, and cardiovascular systems.
- Vascular lesions are common, but cardiac involvement is infrequent.
Findings:
- Cardiac involvement in Behçet's disease is rare.
- This rare complication is linked to a poor prognosis.
Implications:
- Highlights the importance of monitoring for cardiac complications in BD patients.
- Underscores the need for early diagnosis and management of cardiac manifestations.
- Suggests further research into the mechanisms and outcomes of cardiac involvement in BD.
Abstract:
Behçet's disease (BD) is a chronic multisystem disease that presents with recurrent oral and genital ulceration and recurrent uveitis. The patients are often diagnosed in the range of 20-30 years of age and BD are more common in men.[1] BD has a worldwide distribution, but it is mainly observed in Mediterranean areas and Japan.[2] Involvement of skin, joints, nervous, respiratory, gastrointestinal, and cardiovascular systems is also recognised.[34] Although the vascular lesions are frequently observed in this disease, the cardiac involvement is rare and is associated with the poor prognosis.[5].
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