A Case of Myoclonus-Dystonia Responding to Low-frequency Pallidal Stimulation
Harini Sarva1, Joan Miravite2, Matthew C Swan2
1Parkinson's Disease and Movement Disorders Institute, Department of Neurology, Weill Cornell Medicine, New York, NY, USA.
Abstract
Background:
High-frequency pallidal stimulation has been shown to improve various types of dystonia, including myoclonus-dystonia.
Case Report:
We report a case of epsilon sarcoglycan mutation-negative myoclonus-dystonia with response to low-frequency bilateral pallidal stimulation.
Discussion:
Low-frequency pallidal stimulation provides an effective means of treating various dystonias, regardless of genetic status, as in our case, as it provides increased programming options with fewer adverse effects.
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