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Updated: Feb 26, 2026

Three-Dimensional Printing of a Complex Aortic Anomaly
Published on: November 1, 2018
Double aortic arch anomalies in Children: A Systematic 20-Year Single Center Study
M Kaldararova1, I Simkova2, I Varga3
1National Institute of Cardiovascular Diseases-Children's Cardiac Center, Limbova Street 1, Bratislava, 833 51, Slovakia.
This study analyzed 40 pediatric cases of aortic arch anomalies over 20 years. Correctly diagnosing these rare congenital cardiovascular defects, especially ring-forming types, is critical for patient management.
Area of Science:
- Cardiovascular embryology
- Pediatric cardiology
- Congenital cardiovascular defects
Background:
- Aortic arch anomalies are associated with numerous congenital disorders.
- Understanding cardiovascular embryology is essential for diagnosis and treatment.
- A 20-year retrospective analysis was conducted at a national pediatric center.
Purpose of the Study:
- To perform a comprehensive analysis of aortic arch anomalies in a pediatric population.
- To create a catalog of diagnosed aortic arch anomalies.
- To provide epidemiological data on rare congenital cardiovascular defects.
Main Methods:
- Retrospective analysis of 40 pediatric patients diagnosed with aortic arch anomalies.
- Classification into Group 1 (ring-forming) and Group 2 (non-ring-forming) anomalies.
- Morphological analysis using echocardiography, angiography, CT, or MRI.
Main Results:
- Group 1 included 25 patients with ring-forming anomalies (e.g., persistent double aortic arches, right aortic arch with incomplete left arch).
- Group 2 included 15 patients with other aortic arch anomalies, often associated with complex heart defects.
- Incidence of all aortic arch anomalies was 0.033%; ring-forming anomalies were 0.021%.
Conclusions:
- Aortic arch anomalies, though rare, require accurate diagnosis.
- Distinguishing between ring-forming and non-ring-forming types is critical for management.
- This study provides valuable epidemiological data for rare congenital cardiovascular defects.
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