Management of late presentation congenital heart disease

Parvathi U Iyer1, Guillermo E Moreno2, Luiz Fernando Caneo3

  • 11Paediatric Intensive Care Unit,Fortis Escorts Heart Institute,New Delhi,India.

Cardiology in the Young
|December 5, 2017
PubMed

Insights

Timely diagnosis and repair of congenital heart diseases (CHDs) are often unfeasible in low- and middle-income countries. Late presentation of CHDs creates complex challenges for surgical candidacy and perioperative care.

Area of Science:

  • Cardiology
  • Pediatric Surgery
  • Global Health

Background:

  • Timely diagnosis and repair of congenital heart diseases (CHDs) are often not feasible in low- and middle-income countries.
  • Economic development allows for cardiac units managing CHDs presenting later than ideal, missing early stabilization windows.
  • Late presentation can lead to organ dysfunction, pulmonary vascular disease, and sequelae of cyanosis and polycythaemia.

Purpose of the Study:

  • To highlight the challenges associated with late presentation of congenital heart diseases in resource-limited settings.
  • To discuss the clinical and ethical considerations in managing patients with late-presenting CHDs.
  • To inform strategies for surgical candidacy, operative planning, and intensive care for these complex cases.

Main Methods:

  • Review of clinical scenarios and outcomes for patients with late-presenting CHDs.
  • Analysis of challenges in decision-making regarding surgical intervention.
  • Examination of perioperative intensive care management in resource-constrained environments.

Main Results:

  • Late presentation of CHDs is common in low- and middle-income countries.
  • Patients often present with significant organ dysfunction and complications.
  • Decision-making regarding operability and surgical strategy is complex and ethically challenging.

Conclusions:

  • Late presentation of CHDs poses significant clinical and ethical challenges.
  • Effective management requires careful consideration of patient condition, surgical risks, and resource availability.
  • Improved strategies are needed for the timely diagnosis and management of CHDs globally.

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