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Hughes-Stovin syndrome revealing the presence of Behçet's Disease
Melek Kechida1, Sondes Yaacoubi1, Ahmed Zrig2
1Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia.
Background:
Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen.
Case Presentation:
We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet's disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome.
Conclusion:
Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet's disease.
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