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Surgical Treatment of an Endolymphatic Sac Tumor
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Endolymphatic Sac Tumor in von Hippel-Lindau Disease: A Rare Case Report
Rituparna Biswas1, Kalpana Kumari2, Subhash Gupta1
1Department of Radiation Oncology, Dr. BRA IRCH, All India Institute of Medical Sciences, New Delhi, India.
Journal of Pediatric Neurosciences
|December 6, 2017
Abstract:
Endolymphatic sac tumor (ELST) is a rare papillary neoplasm with locally destructive behavior which can occur sporadically or in association with Von Hippel-Lindau (VHL) disease. We herein present a case of ELST associated with VHL disease in a 14-year-old girl and discuss clinico-radiological, immunohistopathologic findings, and management by staged surgery and postoperative radiotherapy to the residual lesion.
