The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report

Louie Ye1, Ernest Lekgabe1, Alpha Tsui2

  • 1Department of Radiology, the Royal Melbourne Hospital, Parkville, VIC, Australia.

Insights

Köhlmeier-Degos disease, a rare vasculopathy, often involves the central nervous system. This case study details 11-year neuroimaging findings, offering new insights into its progression.

Area of Science:

  • Neurology
  • Vascular Biology
  • Rare Diseases

Background:

  • Köhlmeier-Degos disease is a rare idiopathic vasculopathy with unclear pathogenesis.
  • Central nervous system (CNS) involvement in Köhlmeier-Degos disease is uncommon and poorly understood.
  • Longitudinal studies detailing the evolution of neurovascular and neuropathological changes are lacking.

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