Epithelioid Angiosarcoma in Femur: A Case Presentation.

Area of Science:

• Oncology
• Pathology
• Radiology

Background:

• Primary malignant vascular tumors are rare, comprising <1% of primary bone tumors.
• Epithelioid angiosarcoma is an uncommon subtype with an epithelioid phenotype, often mimicking carcinomas.
• These tumors typically occur in extraskeletal locations, with bone involvement being rare.

Observation:

• A 31-year-old male presented with left hip pain.
• Radiography revealed a cystic, expansile mass in the trochanteric region of the femur.
• CT showed a 7 cm cystic mass with septa; MRI suggested an aneurysmal bone cyst.

Findings:

• Histological examination and biopsy confirmed epithelioid angiosarcoma.
• The excised specimen further verified the preoperative diagnosis.
• This case highlights the rarity of epithelioid angiosarcoma in bone.

Implications:

• Accurate diagnosis of epithelioid angiosarcoma requires careful histological evaluation.
• Radiological features can mimic other bone lesions, necessitating a high index of suspicion.
• Understanding rare bone tumor presentations is crucial for effective patient management.