Keratoma hereditaria mutilans: report of a case with successful surgical treatment

A case of constriction band at the fingers arising from keratosis palmoplantaris is reported. Excision of the band and closure of wound by Z-plasties resulted in complete relief of clinical symptoms and vascular insufficiencies. Histologic examination revealed the variability of this skin lesion even in the same patient. The sparsity of keratohyaline matrix in the horn cells in the skin may contribute to the constriction ring formation.