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Implantation of Total Artificial Heart in Congenital Heart Disease
Published on: July 18, 2014
Management of the Critically Ill Adult With Congenital Heart Disease
Wolf B Kratzert1, Eva K Boyd1, Johanna C Schwarzenberger1
1Department of Anesthesiology and Perioperative Medicine, David Geffen School of Medicine at UCLA, Los Angeles, Los Angeles, CA.
Insights
Adults with congenital heart disease (CHD) are increasingly admitted to intensive care units (ICUs) due to long-term complications. Critical care requires understanding complex anatomy and comorbidities for optimal outcomes.
Area of Science:
- Cardiology
- Critical Care Medicine
- Adult Congenital Heart Disease
Background:
- Survival rates for adults with congenital heart disease (CHD) have significantly improved.
- This has led to a rise in hospital and intensive care unit (ICU) admissions for this population.
- Medical emergencies from long-term sequelae of CHD treatment are now more common than perioperative issues.
Purpose of the Study:
- To review the management of critically ill adults with congenital heart disease.
- To discuss the complex anatomy, pathophysiology, and comorbidities associated with CHD.
- To explore adjustments in ICU management and pharmacology for this unique patient group.
Main Methods:
- Review of current literature on adult congenital heart disease critical care.
- Discussion of common CHD lesions and surgical approaches.
- Analysis of long-term sequelae and comorbidities affecting organ systems.
Main Results:
- Adults with CHD present complex anatomical and pathophysiological challenges in the ICU.
- Comorbidities across multiple organ systems (cognitive, pulmonary, cardiovascular, hepatic, renal) are prevalent.
- Contemporary adult ICU care concepts need adaptation for CHD patients.
Conclusions:
- Critical care for adults with CHD demands specialized knowledge of their unique physiology.
- Understanding the interplay of CHD, aging, and comorbidities is crucial for effective management.
- Optimizing ICU care involves tailored management strategies and pharmacology to improve patient outcomes.
Abstract:
Survival of adults with congenital heart disease (CHD) has improved significantly over the last 2 decades, leading to an increase in hospital and intensive care unit (ICU) admissions of these patients. Whereas most of the ICU admissions in the past were related to perioperative management, the incidence of medical emergencies from long-term sequelae of palliative or corrective surgical treatment of these patients is rising. Intensivists now are confronted with patients who not only have complex anatomy after congenital cardiac surgery, but also complex pathophysiology due to decades of living with abnormal cardiac anatomy and diseases of advanced age. Comorbidities affect all organ systems, including cognitive function, pulmonary and cardiovascular systems, liver, and kidneys. Critical care management requires an in-depth understanding of underlying anatomy and pathophysiology in order to apply contemporary concepts of adult ICU care to this population and optimize patient outcomes. In this review, the main CHD lesions and their common surgical management approaches are described, and the sequelae of CHD physiology are discussed. In addition, the effects of chronic comorbidities on the management of critically ill adults are explored, and the adjustments of current ICU management modalities and pharmacology to optimize care are discussed.
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