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Published on: December 15, 2023
Hemifacial spasm secondary to middle ear cholesteatoma
Maheep Sohal1, Nicholas Karter, Marc Eisen
1Division of Otolaryngology-Head and Neck Surgery, University of Connecticut Health Center, 263 Farmington Ave., Farmington, CT 06030, USA. maheep.sohal@gmail.com.
Abstract:
Hemifacial spasm is a peripheral myoclonus of the VIIth cranial nerve that is characterized by paroxysmal contraction of the muscles of facial expression. It exists in both primary and secondary forms. In rare cases, hemifacial spasm is caused by middle ear pathology. We describe the case of a 90-year-old man with recurrent cholesteatoma and tympanic segment fallopian canal dehiscence manifesting as right-sided hemifacial spasm. His history was significant for a right-sided tympanomastoidectomy for cholesteatoma 6 years earlier. Computed tomographic angiography performed to look for vascular compression of the facial nerve demonstrated a right middle ear opacification. Middle ear exploration revealed a completely dehiscent tympanic segment with cholesteatoma abutting the facial nerve. The overlying keratin debris and matrix were carefully dissected off, and facial nerve function was preserved. The final diagnosis was hemifacial spasm. During 14 months of postoperative follow-up, the patient experienced no further facial spasm.
Insights
Hemifacial spasm, a condition affecting facial muscles, can rarely stem from middle ear issues. This case highlights successful treatment of a 90-year-old man whose spasm was caused by recurrent cholesteatoma.
Area of Science:
- Neurology
- Otolaryngology
- Medical Case Study
Background:
- Hemifacial spasm (HFS) involves involuntary contractions of facial muscles, typically due to VIIth cranial nerve irritation.
- While often caused by vascular compression, HFS can rarely be linked to middle ear pathologies.
- Recurrent cholesteatoma and facial nerve involvement present unique diagnostic and management challenges.
Observation:
- A 90-year-old male presented with right-sided hemifacial spasm.
- He had a history of middle ear cholesteatoma treated surgically six years prior.
- Imaging revealed recurrent cholesteatoma and dehiscence of the tympanic segment of the facial canal.
Findings:
- Middle ear exploration confirmed cholesteatoma abutting a dehiscent facial nerve.
- Surgical dissection of the cholesteatoma and matrix preserved facial nerve function.
- The patient's hemifacial spasm resolved postoperatively.
Implications:
- This case highlights middle ear cholesteatoma as a treatable cause of hemifacial spasm.
- It underscores the importance of considering otologic pathology in secondary HFS cases.
- Successful surgical management can restore facial nerve function and alleviate spasm.
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