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Impact of unilateral congenital aural atresia on academic Performance: A systematic review
C V A van Hövell Tot Westerflier1, J A A van Heteren2, C C Breugem1
1Department of Pediatric Plastic Surgery, Wilhelmina Children's Hospital, University Medical Center Utrecht, Lundlaan, 6, 3584, EA, Utrecht, The Netherlands.
Insights
Academic performance in children with unilateral congenital aural atresia (CAA) is poorly understood. Current evidence is limited and biased, highlighting the need for high-quality studies on this hearing loss condition.
Area of Science:
- Otolaryngology
- Pediatric Audiology
- Developmental Pediatrics
Background:
- The academic performance of children with unilateral congenital aural atresia (CAA) is not well-documented.
- Unilateral hearing loss due to CAA may impact a child's educational development.
Purpose of the Study:
- To systematically review existing literature on the academic performance of children with unilateral CAA.
- To provide recommendations for clinicians managing these children.
Main Methods:
- A systematic search of PubMed, EMBASE, and Cochrane Library was conducted.
- Included observational studies on academic achievement in patients with unilateral conductive hearing loss from CAA.
- Outcome measures included grade retention, special education, and individualized education plans.
Main Results:
- Only two studies reported academic performance data for unilateral CAA, both with significant risk of bias.
- One study indicated 3.6% grade retention, 15.7% special education, and 36.4% individualized education program use.
- The second study found 29.9% received school intervention and 25.4% had learning problems.
Conclusions:
- Evidence on the academic impact of unilateral CAA is sparse, inconclusive, and prone to bias.
- High-quality observational studies are needed to accurately assess the effects of CAA on academic performance.
Background:
Little is known about the academic performance of children with unilateral congenital aural atresia (CAA).
Objective:
of review: Our objective was to summarize what is known about the academic performance of children with hearing loss by unilateral congenital aural atresia, in order to provide pragmatic recommendations to clinicians who see children with this entity.
Type Of Review:
Systematic review.
Search Strategy:
We conducted a systematic search in PubMed Medline, EMBASE, and Cochrane Library combining the terms "atresia" and synonyms with "unilateral hearing loss" and synonyms. Date of the most recent search was 16 May 2018.
Evaluation Method:
Two independent authors identified studies, extracted data, and assessed risk of bias. This review was reported according to the Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA). Observational studies on the academic achievements of patients of any age with unilateral conductive hearing loss of any level due to congenital aural atresia were included. We considered grade retention, special education, individualized education plans, and parental report of school performance as outcome measures for academic achievement.
Results:
Two studies reporting on academic performance of patients with unilateral CAA, which both had a significant risk of bias. One study (n = 140) showed a grade retention rate of 3.6% (n = 5) in total. 15.7% (n = 22) needed special education, and 36.4% (n = 51) used an individualized education program. The second study, reporting on 67 patients with unilateral CAA, showed that 29.9% (n = 20) of the patients received school intervention, and 25.4% (n = 17) had learning problems.
Conclusion:
Current evidence regarding the effect of unilateral congenital aural atresia on academic performance is sparse, inconclusive and has a significant risk of bias. High quality observational studies assessing the effects of aural atresia on academic performance in these patients should be initiated.
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