Pancreatic heterotopia in a neonatal abdominopelvic cyst

Pancreatic heterotopia is a rare congenital anomaly more commonly incidentally found in adults. While intra-abdominal cysts found on prenatal imaging are not uncommon, we examine a case of pancreatic heterotopia presenting in an abdominopelvic cyst on prenatal imaging. At birth, the neonate was found to have hypoglycemia unresponsive to treatment that resolved after cyst resection. We will review the etiology, imaging findings and clinical course of this anomaly, which should be considered in the differential diagnosis of newborns presenting with unexplained hypoglycemia.