[Initial description of a retinal ganglioglioma]

Gangliogliomas are very rare neuronal tumors, predominantly localized in the thalamus, third ventricle, and temporal lobe. They usually occur in younger patients, grow slowly, and their glial components may develop to malignancy. A case is reported in which a tumor was detected on the upper rim of the optic disk. The patient was then four years old. Five years later the eye hat to be enucleated because of increasing growth and vascularization of the tumor. Histologically, it consisted of mature ganglion cells and neoplastic glial cells. Six years later, in addition to the glial hamartoma, a vascular hamartoma, i.e., a hemangioblastoma of the cerebellum, was found, this tumor was extirpated.