Truncus Arteriosus With Major Aortopulmonary Collateral Arteries

Area of Science:

• Cardiovascular Surgery
• Pediatric Cardiology
• Congenital Heart Disease

Background:

• Truncus arteriosus is a rare congenital heart defect.
• Absence of a pulmonary artery branch and presence of major aortopulmonary collateral arteries (MAPCAs) represent a complex anatomical variant.
• Early diagnosis and surgical intervention are critical for patient outcomes.

Observation:

• A neonate presented with a rare form of truncus arteriosus.
• The condition included the absence of the left pulmonary artery and the presence of MAPCAs.
• The patient had a low birth weight of 2,219 g.

Findings:

• A staged surgical approach was successfully employed for repair.
• Key procedures included banding of the left pulmonary artery and unifocalization of MAPCAs.
• The surgical intervention achieved successful repair in this complex case.

Implications:

• This case demonstrates the feasibility of a staged surgical strategy for complex truncus arteriosus.
• Pulmonary artery banding and MAPCAs unifocalization are crucial techniques in managing such anomalies.
• Successful repair in neonates with complex congenital heart disease highlights advancements in pediatric cardiac surgery.