Partial anomalous pulmonary venous return: A case series with management approach

Area of Science:

• Cardiology
• Congenital Heart Disease
• Pulmonology

Background:

• Partial anomalous pulmonary venous return (PAPVR) is a rare congenital heart defect characterized by abnormal pulmonary venous connection.
• It leads to a left-to-right shunt, with clinical presentation varying based on shunt volume.

Observation:

• Unrepaired significant shunts can cause pulmonary vascular remodeling and pulmonary arterial hypertension (PAH).
• Co-occurrence with atrial septal defects (ASD) may precipitate shunt reversal and Eisenmenger's syndrome in severe PAH cases.

Findings:

• This study presents diverse clinical cases of PAPVR.
• Individualized management strategies are crucial for optimal outcomes.

Implications:

• Early recognition and management of PAPVR are vital to prevent progression to PAH and Eisenmenger's syndrome.
• Treatment approaches, including observation, surgical correction, and pharmacotherapy, should be tailored to each patient's specific presentation and shunt severity.