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Published on: January 14, 2014
[Paraganglioma of Zuckerkandl's organ. Report of two pediatric cases]
V Medina Gaviria1, L Rodríguez Romero1, I Molina Ramírez1
1Servicio de Cirugía Pediátrica. Universidad Nacional de Colombia-Fundación Hospital Pediátrico de la Misericordia (HOMI). Colombia.
Introduction:
Pheochromocytoma is an infrequent neuroendocrine tumor, originated from neural crest cells. 10% of them are extra adrenal, located at sympathetic nodules and are known as paragangliomas. The most common place is the Zuckerkandl organ, 10 to 26% are malign and has a mortality around de 26% of the cases.
Case Report:
We present two cases of teenagers with Zuckerkandl's organ paraganglioma, who debut with high blood pressure, diaphoresis and dyspnea. Complete tumor resection was performed in both cases, during which they presented hipertensive crisis and, after vascular pedicle ligation, hypotension.
Conclusions:
Zuckerkandl's organ paraganglioma is a rare pathology in pediatric population, therefore represents an important diagnostic and therapeutic challenge. Surgery differs from other tumors because of catecholamine secretion that produces hemodynamic changes and demands prompt and accurate management from surgeon and anesthetist.
