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Fatal nodular xanthomatosis in an infant
R Caputo1, E Ermacora, C Gelmetti
1Institute of Clinical Dermatology and Pediatric Dermatology, University of Milan, Italy.
Pediatric Dermatology
|November 1, 1987
Abstract:
We describe a unique and puzzling case of a 7-month-old baby with a non-X hypertriglyceridemic histiocytoxanthomatosis. The disease was characterized by a massive nodular eruption that was clinically, histologically, and ultrastructurally consistent with juvenile xanthogranuloma, but it had a rapid, fatal evolution.