The long-term outcome of an isolated vascular ring - A single-center experience

Anouk Depypere1, Marijke Proesmans1, Björn Cools2

  • 1Department of Pediatrics, Pediatric Pulmonology, University Hospital Leuven, Leuven, Belgium.

Pediatric Pulmonology
|August 29, 2019
PubMed

Insights

Long-term outcomes for congenital vascular ring patients show surgery is safe, but many retain symptoms like stridor. Conservative management may suit less symptomatic individuals.

Area of Science:

  • Pediatric Surgery
  • Cardiovascular Surgery
  • Medical Diagnostics

Background:

  • Congenital vascular rings are rare anomalies affecting the great arteries.
  • Long-term outcomes and symptom resolution following treatment are not well-documented.

Purpose of the Study:

  • To document the long-term clinical outcomes of patients diagnosed with a complete vascular ring.
  • To evaluate the effectiveness of surgical and conservative management strategies.

Main Methods:

  • Retrospective review of 51 patients diagnosed with complete vascular rings between 1980-2013.
  • Data collected included age at diagnosis, diagnostic tools, surgical procedures, complications, and long-term symptoms via parental questionnaires.
  • Follow-up duration was at least 2 years, with a median of 8 years.

Main Results:

  • Surgery was performed in 41 patients, primarily for double aortic arch, with few reversible complications.
  • After 2 years, 21 patients were asymptomatic, while 30 continued to experience symptoms, with varying degrees of improvement or worsening.
  • After 10 years, 26/36 patients were symptom-free, with stridor being the most frequent residual symptom.

Conclusions:

  • Surgical treatment for congenital vascular rings, especially double aortic arches, is safe and effective.
  • Conservative management may be appropriate for patients with minimal symptoms.
  • A significant proportion of patients experience persistent long-term symptoms even after surgical intervention.
Abstract

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