LRRK2 Biology from structure to dysfunction: research progresses, but the themes remain the same

Daniel C Berwick1, George R Heaton2, Sonia Azeggagh3

  • 1School of Health, Life and Chemical Sciences, The Open University, Walton Hall, Milton Keynes, MK7 6AA, UK. daniel.berwick@open.ac.uk.

Molecular Neurodegeneration
|December 23, 2019
PubMed

Insights

Leucine-rich repeat kinase 2 (LRRK2) is implicated in Parkinson's disease. This review details LRRK2's cellular functions, including its kinase and GTPase activities, and roles in various cellular processes and organelles.

Area of Science:

  • Biochemistry
  • Cell Biology
  • Neuroscience

Background:

  • Leucine-rich repeat kinase 2 (LRRK2) is a key protein implicated in Parkinson's disease etiology.
  • Extensive research has focused on understanding LRRK2's fundamental cellular functions and its involvement in diverse biological pathways.

Purpose of the Study:

  • To review current knowledge on the basic biochemistry and cellular functions of LRRK2.
  • To summarize advances in understanding LRRK2's kinase and GTPase activities, activation mechanisms, and roles in cellular processes.

Main Methods:

  • Review of existing literature on LRRK2 biochemistry and cell biology.
  • Analysis of studies identifying LRRK2 phosphorylation substrates (e.g., Rab proteins).
  • Examination of research on LRRK2 activation, dimerization, membrane association (e.g., with Rab29), and GTPase activity.

Main Results:

  • LRRK2 kinase activity phosphorylates substrates like Rab proteins.
  • LRRK2 activation involves dimerization, membrane association (particularly with Rab29), and complex GTPase activity.
  • LRRK2 is linked to diverse cellular functions including autophagy, endocytosis, and organelle biology (trans-Golgi network, endoplasmic reticulum, microtubules).

Conclusions:

  • LRRK2 plays multifaceted roles in cellular signaling and organelle dynamics.
  • A proposed mechanism links LRRK2 dimerization, GTPase function, membrane recruitment, and Rab29-mediated kinase activation.
  • Despite significant advances, the fundamental understanding of LRRK2's complex roles continues to evolve.

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