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Cardiac Rhabdomyoma Causing Progressive Dynamic Severe Right Ventricular Outflow Tract Obstruction in an Infant
Amitabh Poonia1, Priya Giridhara2, Arun Gopalakrishnan2
1Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, Kerala, India. amitabhpoonia@gmail.com.
Indian Pediatrics
|February 16, 2020
Summary
Cardiac rhabdomyoma, a rare tumor, can cause severe heart obstruction in infants. Surgical removal of these intracardiac masses can be life-saving, relieving symptoms and improving outcomes in affected neonates.
Area of Science:
- Pediatric Cardiology
- Cardiac Oncology
- Neonatal Medicine
Background:
- Cardiac rhabdomyomas are benign tumors that can arise in the heart of neonates.
- While often asymptomatic, they can lead to significant cardiovascular complications.
- Early detection and intervention are crucial for managing potential adverse outcomes.
Observation:
- Multiple cardiac masses were incidentally found in a neonate.
- At seven months, the infant presented with failure to thrive, feeding difficulties, and severe dynamic right ventricular outflow tract obstruction.
- These symptoms indicated significant hemodynamic compromise due to the cardiac masses.
Findings:
- Surgical resection of the intracardiac masses was performed.
- Histological examination confirmed the diagnosis of cardiac rhabdomyoma.
- The tumor exhibited progressive growth during infancy, an uncommon clinical presentation.
Implications:
- Surgical intervention effectively relieved the infant's symptoms and obstruction.
- This case highlights that even rapidly growing cardiac rhabdomyomas can be successfully treated with surgery.
- Prompt surgical management of symptomatic cardiac rhabdomyomas can be life-saving in neonates and infants.
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