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[Cystic fibrosis, what follow-up action for adults in 2019?]

Juliette Champreux1

  • 1Hôpital Cochin, 27, rue du Faubourg- Saint-Jacques, 75014 Paris, France.

Revue De L'Infirmiere
|March 10, 2020
PubMed

Insights

Cystic fibrosis (CF) now affects more adults than children in France, shifting its classification from a pediatric to an adult pathology. This demographic change necessitates evolving healthcare strategies to meet the emerging needs of adult CF patients.

Area of Science:

  • Pulmonology
  • Genetics
  • Epidemiology

Background:

  • Cystic fibrosis (CF) was historically viewed as a pediatric disease.
  • Recent data indicates a demographic shift in France, with adult CF cases now exceeding pediatric cases since 2015.
  • This epidemiological transition highlights evolving patient demographics in CF care.

Purpose of the Study:

  • To analyze the implications of the increasing adult population with cystic fibrosis.
  • To underscore the need for adapting healthcare organization for adult CF patients.
  • To identify emerging healthcare needs in the adult CF population.

Main Methods:

  • Demographic analysis of cystic fibrosis patient data in France.
  • Review of healthcare organization models for chronic diseases.
  • Identification of specific needs in adult patient care pathways.

Main Results:

  • Since 2015, adults represent the majority of the cystic fibrosis population in France.
  • The shift necessitates a re-evaluation of healthcare structures and resource allocation.
  • New and specific healthcare needs are emerging within the adult CF population.

Conclusions:

  • Cystic fibrosis is transitioning into a predominantly adult disease in France.
  • Healthcare systems require significant adaptation to address the evolving needs of adults with CF.
  • Proactive planning is crucial for optimizing adult CF care and improving patient outcomes.

Keywords:
adultadultecystic fibrosismanagementmucoviscidoseparcours patientpatient journeyprise en chargequality of lifequalité de vie

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