Dysplasia epiphysealis hemimelica at the metacarpophalangeal joint

Dysplasia epiphysealis hemimelica (DEH) or Trevor's disease is a rare developmental disorder of asymmetric epiphyseal cartilage overgrowth accompanied by an accessory, epiphyseal ossification center. No published reports exist of metacarpal or phalangeal DEH. We report a case of bilateral DEH of the index finger: right-sided distal index metacarpal and left-sided index proximal phalanx. Both were surgically corrected with excision of the accessory ossification center; a transepiphyseal cartilaginous wedge was excised, and the articular surface was maintained. Follow-up shows maintenance of alignment without recurrence at 12 and 18 months after operation.