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Audiologic evaluation in Charcot-Marie-Tooth disease
H Pérez1, J Vílchez, T Sevilla
1Department of Otolaryngology and Neurology, Hospital La Fe, Valencia, Spain.
Scandinavian Audiology. Supplementum
|January 1, 1988
Abstract:
We have carried out a hearing study with pure tone audiometry and ABR of 39 patients affected by hereditary motor and sensory neuropathy or Charcot-Marie Tooth disease. We have noticed a hearing deficiency in a significant percentage of cases (28%). We attribute the abnormalities to disorders in the area of the VIIIth nerve and of the brainstem. No significant differences appear in the results obtained between patients belonging to type I and patients belonging to type II of this disease.