Exercise testing for children with cystic fibrosis: A systematic review
Ray Lei Lang1, Kellie Stockton2, Christine Wilson2
1School of Health and Rehabilitation Sciences, The University of Queensland, St Lucia, Australia.
Pediatric Pulmonology
|May 27, 2020
Summary
This review assesses exercise tests for children with cystic fibrosis (CF), finding the cardiopulmonary exercise test (CPET), 6-minute walk test (6MWT), and modified shuttle test (MST) offer fair to good psychometric properties.
Area of Science:
- Pediatric Pulmonology
- Exercise Physiology
- Rehabilitation Science
Background:
- Exercise testing is crucial for assessing exercise capacity in pediatric cystic fibrosis (CF) patients.
- A systematic review of psychometric properties of available exercise tests for this population was lacking.
Purpose of the Study:
- To systematically review the psychometric properties of exercise tests used in children aged 8-18 with CF.
- To provide guidance for selecting appropriate exercise tests for this population.
Main Methods:
- A systematic literature search was conducted across multiple databases (PubMed, Web of Science, etc.) for studies published after 1950.
- Included studies reported original psychometric data for exercise capacity measures in children with CF (ages 8-18).
- The COnsensus-based Standards for the selection of health Measurement INstruments (COSMIN) checklist was used to evaluate psychometric evidence.
Main Results:
- 1025 papers were identified, with 46 included, covering 15 different exercise tests.
- Tests included incremental cardiopulmonary exercise test (CPET) via cycle or treadmill, 6-minute walk test (6MWT), modified shuttle test (MST), and others.
- The CPET, 6MWT, and MST demonstrated fair to good psychometric properties, though each has unique clinical benefits and drawbacks.
Conclusions:
- A wide range of exercise tests exist for pediatric CF patients, with variable psychometric quality.
- The CPET, 6MWT, and MST are recommended due to their relatively robust psychometric evidence.
- A Selection Guide was developed to aid clinicians and researchers in choosing the most suitable exercise test based on specific needs.
Keywords:
cardiopulmonary exercise testingchildren exercise stress testingphysiotherapy in cystic fibrosisMore Related Videos
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