Related Experiment Videos
Dermochondrocorneal dystrophy (François' syndrome). Report of a case
R Caputo1, N Sambvani, M Monti
1Institute of I Dermatologic Clinic, University of Milan, Italy.
Archives of Dermatology
|March 1, 1988
Abstract:
Dermochondrocorneal dystrophy (François' syndrome) is an extremely rare disorder characterized by firm, nodular lesions involving the hands and the face; osteochondrodystrophy of the peripheral extremital bones, resulting in limitation of movement; and corneal dystrophy marked by white or brownish opacities. A nonfamilial case of dermochondrocorneal dystrophy was studied in a 45-year-old woman who had severe involvement of the gingival and palatal mucous membranes.