Nerve Sheath Myxoma: A rare tumor, a case report and literature review

Nerve Sheath Myxoma is a rare benign nerve sheath tumor, commonly seen in young adults. Patients usually present with a small nodule commonly affecting upper and lower limbs. Nerve Sheath Myxoma has not been reported in children below the age of 1 year.

We present the first reported case of Nerve Sheath Myxoma (NSM) in the hand in a 4-month old child in line with the SCARE 2018 criteria.

NSM is difficult to diagnose using standard imaging technique; Magnetic Resonance Imaging (MRI) and Ultrasonography (USS) cannot differentiate it from vascular anomalies.

Soft tissue tumors in the hand of pediatric population are difficult to diagnose. Formal excision of the tumor by a specialized pediatric hand surgeon and histopathological analysis were the only avenue to correctly diagnose the NSM.