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Direct Re-implantation of Left Coronary Artery into the Aorta in Adults with Anomalous Origin of Left Coronary Artery from the Pulmonary Artery ALCAPA
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Primary and secondary aortopathy associated with adult congenital heart disease - retrospective study

Ingrid Schusterova1, Alžbeta Banovcinova2, Marianna Vachalcova1

  • 11th Department of Cardiology, East Slovak Institute of Cardiovascular Diseases, Faculty of Medicine, Pavol Jozef Safarik University in Kosice, Kosice, Slovakia.

Journal of Cardiothoracic Surgery
|September 11, 2020
PubMed

Insights

Adults with congenital heart disease and aortopathy, particularly secondary aortopathy, show significantly larger aortic diameters. Regular monitoring of aortic size is crucial for these patients.

Area of Science:

  • Cardiovascular Medicine
  • Adult Congenital Heart Disease
  • Aortopathy

Background:

  • Aortopathy is a common complication in adult patients with congenital heart disease (CHD).
  • Understanding the incidence and characteristics of primary and secondary aortopathy in this population is essential.

Purpose of the Study:

  • To investigate the incidence and clinical features of primary and secondary aortopathy in adult CHD patients.
  • To compare aortic dimensions between patients with and without aortopathy, and between primary and secondary aortopathy groups.

Main Methods:

  • Retrospective analysis of adult CHD patients from a specialized registry.
  • Inclusion of 35 patients with primary aortopathy, 12 with secondary aortopathy, and 64 controls with non-aortopathy CHD.
  • Comparison of aortic root and ascending aorta diameters using follow-up data.

Main Results:

  • Patients with primary and secondary aortopathy exhibited significantly larger ascending aorta and aortic root diameters compared to controls.
  • Secondary aortopathy patients demonstrated statistically larger ascending aorta diameters than primary aortopathy patients.
  • Aortic root and ascending aorta operations were infrequent during follow-up.

Conclusions:

  • Secondary aortopathy in adult CHD patients is associated with more pronounced dilation of the ascending aorta and aortic root.
  • Routine surveillance of aortic diameters is recommended for adult CHD patients with aortopathy.
Abstract

Keywords:
Aortic rootAscending aortaCongenital heart diseasePrimary/secondary aortopathy

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