Cicatricial ectropion correction for a case of amniotic band syndrome

S M Balaji1, Preetha Balaji1

  • 1Department of Oral and Maxillofacial Surgery, Balaji Dental and Craniofacial Hospital, Chennai, Tamil Nadu, India.

Insights

A rare case of amniotic band syndrome (ABS) involving craniofacial deformities, specifically Tessier Cleft-9 and Cleft-2 with ectropion, is presented. Management requires staged surgical correction and careful monitoring due to dynamic growth.

Area of Science:

  • Congenital malformations
  • Developmental biology
  • Craniofacial surgery

Background:

  • Amniotic band syndrome (ABS), also known as amniotic deformity, adhesions and mutilations (ADAM), is a rare spectrum of congenital malformations.
  • ABS can manifest in various forms within the craniofacial region.
  • This report details a rare presentation of ABS involving Tessier Cleft-9 and atypical Cleft-2.

Observation:

  • The observed case presented with a cicatricial ectropion.
  • This specific combination of clefts and ectropion represents a rare manifestation of ABS.
  • The craniofacial components of ABS necessitate a deep understanding of growth and healing principles.

Findings:

  • Surgical management of ABS-related oro-facial deformities is complex and requires staged correction.
  • The dynamic nature of growth means that problems can evolve, necessitating anticipation.
  • Early intervention and frequent follow-up are crucial to prevent complications.

Implications:

  • Effective surgical planning for ABS requires a thorough understanding of pediatric craniofacial growth and wound healing.
  • Staged surgical correction and vigilant post-operative care are essential for optimal outcomes in ABS patients.
  • Anticipating evolving issues and intervening early can mitigate unfavorable complications in managing these rare congenital conditions.
Abstract