Pediatric bronchiectasis: An orphan disease ending in pneumonectomy: A case report
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Published on: July 10, 2012
Esubalew Taddese Mindaye1, Goytom Knfe Tesfay2, Maru Gama Erge2
1Department of Surgery, Saint Paul's Hospital Millennium Medical College, Swaziland Street 1271, Addis Ababa, Ethiopia.
Insights
Pediatric bronchiectasis, a chronic lung disease, requires prompt diagnosis and intervention to prevent severe complications. Early recognition of symptoms like persistent cough is vital for effective management and improved outcomes in children.
Area of Science:
- Pediatric Pulmonology
- Respiratory Medicine
- Clinical Case Study
Background:
- Bronchiectasis is a chronic inflammatory lung disease causing irreversible airway damage and reduced lung function in children.
- Early diagnosis and multidisciplinary care are essential for managing exacerbations and preserving lung function.
Observation:
- A 10-year-old female presented with a 5-week history of wet cough, low-grade fever, shortness of breath, fatigue, and appetite loss.
- The patient underwent a left pneumonectomy via left posterolateral thoracotomy and was discharged in stable condition.
Findings:
- Common causes of pediatric bronchiectasis include recurrent infections, primary immune deficiency, ciliary dyskinesia, foreign body aspiration, and structural abnormalities.
- High Resolution Computerized Tomography (HRCT) is the diagnostic standard for bronchiectasis severity assessment.
Implications:
- Delayed diagnosis in children, often due to atypical symptoms, leads to significant morbidity and mortality.
- Surgical resection is a last resort for refractory cases of pediatric bronchiectasis unresponsive to medical management.
Introduction:
Bronchiectasis is chronic infectious and inflammatory disease that results in irreversible thickening and dilatation of bronchi, and significant lung function decline in children. Prompt early diagnosis and multidisciplinary intervention is crucial to control recurrent exacerbation and preserve lung function.
Presentation Of Case:
We present a case of pediatric bronchiectasis in a 10-year-old female who presented with a complaint of intermittent wet cough of 5 weeks' duration associated with low grade intermittent fever, shortness of breath, easy fatigability and loss of appetite. Left pneumonectomy was done through left posterolateral thoracotomy and she was discharged home in good condition.
Discussion:
Recurrent lower tract air way infections are the most common causes of pediatric bronchiectasis followed by primary immune deficiency, primary ciliary dyskinesia, foreign body aspiration and airway structural abnormalities. It is crucial to equip health care professionals with adequate knowledge about the disease as most pediatric patients may not have productive cough like adults leading to misdiagnosis or significant delay in diagnosis. High Resolution Computerized Tomography (HRCT) is the gold standard modality to diagnose and stratify severity of bronchiectasis.
Conclusion:
Neglected pediatric bronchiectasis is associated with significant morbidity and mortality. So, it should be considered as differential diagnosis in children with recurrent respiratory symptoms as timely and prompt diagnosis is crucial for early intervention. Surgical resection is the last option of treatment for patients with bronchiectasis mainly reserved for those with recurrent infection despite adequate medical therapy.
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