Related Experiment Video
Updated: Nov 16, 2025
Author Spotlight: Studying Clinical Characters and Epilepsy Outcomes After Frontal Disconnection in Patients with MOGHE
Published on: August 16, 2024
Moyamoya Disease-"A Puff of Smoke": A Rare Pediatric Case Report
Mridula Goswami1, Ramanandvignesh Pandian1, Sadhna Sharma1
1Department of Pedodontics and Preventive Dentistry, Maulana Azad Institute of Dental Sciences, New Delhi, India.
Introduction:
Moyamoya disease (MMD) is a rare neurovascular disorder that is characterized by chronic progressive stenosis at the apices and bilateral occlusion of the intracranial internal carotid arteries. The occlusion is gradual in manner; multiple anastomoses are formed between the internal and external carotid arteries. The incidence of MMD has increased in Asian countries with a decline in Europe and United States.
Case Description:
The case report describes the specific clinical features and dental treatment in a 12-year-old male presenting with MMD with right-side hemiplegia. The patient presented with broken tooth in the upper front tooth region due to trauma. The dental treatment plan focused on providing restorative as well as preventive care to the patient.
Clinical Significance:
The patients with MMD have an increased risk of stroke development, which may be aggravated by pain or anxiety. It is necessary to avoid cerebral ischemic attacks caused by fluctuating BP and respiration. It becomes imperative to maintain normocapnia, normotension, and pain control during the procedure in order to prevent postoperative ischemic complications. Dental professionals must attain a complete knowledge of this disease and perform the dental treatment in pain and stress-free manner.
How To Cite This Article:
Goswami M, Pandian R, Sharma S. Moyamoya Disease-"A Puff of Smoke": A Rare Pediatric Case Report. Int J Clin Pediatr Dent 2020;13(5):566-568.
Insights
Moyamoya disease (MMD) is a rare condition causing progressive stenosis of brain arteries. Dental treatment for a child with MMD focused on restorative and preventive care, emphasizing pain and stress-free management to avoid stroke complications.
Area of Science:
- Neurology
- Pediatric Dentistry
- Vascular Medicine
Background:
- Moyamoya disease (MMD) is a rare, progressive neurovascular disorder characterized by stenosis of intracranial carotid arteries.
- It involves the formation of collateral vessels between internal and external carotid arteries, with increasing incidence in Asian populations.
- MMD poses a significant risk for cerebrovascular events like stroke.
Observation:
- This case report details the dental management of a 12-year-old male with MMD presenting with right-side hemiplegia.
- The patient required restorative and preventive dental care for a fractured anterior tooth.
- The clinical scenario highlights the intersection of MMD and pediatric dental care.
Findings:
- Dental treatment for MMD patients requires careful consideration of their heightened stroke risk.
- Restorative and preventive dental strategies were implemented to address the patient's dental trauma.
- The case underscores the need for meticulous dental planning in patients with MMD.
Implications:
- Dental professionals must possess comprehensive knowledge of MMD to ensure patient safety.
- Managing pain and anxiety is crucial to prevent blood pressure fluctuations and avoid ischemic events.
- A pain-free, stress-free dental approach is imperative for MMD patients to prevent postoperative complications.
Related Concept Videos
01:22Mitral Stenosis I: Introduction
01:23Mitral Stenosis II: Clinical features and Diagnostic Tests
01:21Aneurysm II: Clinical Manifestations and Diagnostic Studies
01:26Mitral Stenosis III: Medical Management
01:25Cardiomyopathy I: Introduction and Classification
01:30Coronary Artery Disease III: Clinical Manifestations