Acyanotic Truncus Arteriosus: Not a Misnomer But a True Rarity
Subramanian Chellappan1, Krishna Manohar2, Yogesh Sathe3
1Department of Paediatric Cardiac Anaesthesia, Sri Sathya Sai Sanjeevani International Centre for Child Heart Care and Research, Palwal, Haryana, India.
Summary
Truncus arteriosus (TA) is a congenital heart defect. A 13-year-old boy with type 1 TA presented without cyanosis, enabling successful surgical repair.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Truncus arteriosus (TA), or common arterial trunk (CAT), is a rare cyanotic congenital heart disease.
- It involves a single arterial trunk supplying both pulmonary and systemic circulations.
- Cyanosis typically results from the admixture of oxygenated and deoxygenated blood.
Observation:
- A 13-year-old boy with type 1 TA was observed.
- Notably, the patient presented without cyanosis.
- He exhibited characteristics suitable for surgical intervention at this age.
Findings:
- The patient underwent successful surgical repair of type 1 TA.
- The procedure included closure of a subtruncal ventricular septal defect (VSD).
- A hand-sewn valved conduit (bovine pericardium and Gore-Tex) was implanted between the right ventricle and pulmonary artery.
Implications:
- This case highlights that Truncus Arteriosus can be operable even in late adolescence.
- Successful repair in acyanotic patients demonstrates the importance of individualized assessment.
- The use of a valved conduit is a viable surgical strategy for TA repair.
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