[Bilateral kidney cancer in a patient with Von Hippel-Lindau disease]

A case of bilateral renal carcinoma in a female patient presenting with Von-Hippel-Lindau disease is reported. Many different lesions may be associated in this autosomal dominant disease and the presence of renal involvement must be investigated in every patient. Renal carcinoma, often bilateral, is now frequently treated by conservative methods. It is always necessary to conduct an epidemiological survey in the entire family.