A rare coronary anomaly as a possible cause of ventricular tachycardia
Javier Cuevas-Pérez1, Rodrigo Fernández1, Yván R Persia-Paulino1
1Servicio de Cardiología, Hospital Universitario Central de Asturias, Oviedo, España.
Insights
A rare coronary artery anomaly, presenting as absent left main coronary artery and unusual origins for the anterior descending and circumflex arteries, was found incidentally. This case highlights diagnostic challenges and the importance of recognizing such congenital heart variations.
Area of Science:
- Cardiology
- Anatomical Pathology
- Medical Imaging
Background:
- Coronary artery anomalies are congenital variations in the origin or course of coronary arteries.
- These anomalies can range from benign to life-threatening, often presenting diagnostic challenges.
- Early identification is crucial for appropriate management and prevention of adverse cardiac events.
Observation:
- A 77-year-old male presented with syncope due to sustained monomorphic ventricular tachycardia.
- Coronary angiography revealed an absent left main coronary artery with independent origins for the circumflex and anterior descending arteries from the right coronary sinus.
- Computed tomography with 3D reconstruction confirmed these findings, along with an interarterial path for the anterior descending artery and a retro-aortic path for the circumflex artery.
Findings:
- The patient had an unusual coronary artery anomaly characterized by the absence of the main coronary artery.
- Specific findings included independent ostial origins for the circumflex and anterior descending arteries, an interarterial course of the anterior descending artery, and a retro-aortic course of the circumflex artery.
- These anatomical variations were identified as an incidental finding during the workup for ventricular tachycardia.
Implications:
- This case underscores the diagnostic complexity of coronary artery anomalies, which are often discovered incidentally.
- Recognition of such rare anatomical variations is vital for understanding their potential contribution to cardiac arrhythmias, especially in younger patients.
- Implantation of an implantable cardioverter defibrillator provided secondary prevention, leading to a favorable outcome and discharge without incident.
Abstract:
We present the case of a 77-year-old man who came to the emergency room after a syncopal episode in the context of sustained monomorphic ventricular tachycardia for which electrical cardioversion was performed. In order to determine the etiology of the ventricular arrhythmic event, a study of the coronary anatomy was carried out using invasive coronary angiography, observing coronary arteries without significant lesions, although, as a chance finding, a coronary anomaly was described, with absence of the main coronary artery, with independent exit of circumflex (Cx) and anterior descending (AD) arteries of the right coronary sinus, originating the AD and right coronary artery from the same coronary ostium. These findings were later confirmed by computed tomography with 3D reconstruction. In addition, an interarterial path of AD (between aorta and pulmonary artery) and an intramuscular path of AD were observed, as well as a retro-aortic path of Cx. Given these findings, an implantable cardioverter defibrillator was implanted as secondary prevention. Good subsequent evolution with home discharge without incident. We present this case to help better understand these disorders, since they currently constitute a diagnostic challenge, since in many cases it is a chance finding in complementary tests or even in autopsies. It is also a relatively frequent cause of cardiorespiratory arrest in young patients. Of the many anatomical variables that make up the group of coronary anomalies, there is little bibliographic information on this anomaly presented, without finding images similar to those reported in this case.
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