Related Experiment Video
Updated: Oct 16, 2025

Novel and Innovative Hybrid Technique for Type A Aortic Dissection
Published on: March 28, 2025
Atypical Shone's Complex Diagnosed at 70 Years Old: Presenting with Double-orifice Mitral Valve, Bicuspid Aortic
Tomohiro Kaneko1, Sakiko Miyazaki1, Takuma Koike1
1Department of Cardiovascular Biology and Medicine, Juntendo University Graduate School of Medicine, Japan.
Insights
Atypical Shone's complex, a rare heart defect, can present later in life. This case highlights the importance of diagnosing multiple cardiovascular anomalies in older adults.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiovascular Surgery
Background:
- Atypical Shone's complex involves multiple left-sided heart obstructions.
- Bicuspid aortic valves are often associated with other congenital heart defects.
Abstract:
Atypical Shone's complex is a rare congenital anomaly involving a left-sided obstructive lesion of two or three cardiovascular levels. A 70-year-old man with dyspnea on exertion was diagnosed with severe aortic stenosis (AS) with a bicuspid valve, complicated by severe aortic coarctation (CoA) and a double-orifice mitral valve. He underwent surgery for AS and CoA in one session. It is important to search for complicated malformations, even in cases of bicuspid aortic valve found in old age.
Related Concept Videos
Mitral Stenosis I: Introduction
Mitral Stenosis II: Clinical features and Diagnostic Tests
Aortic Regurgitation II: Clinical Features and Diagnostic Tests
Mitral Valve Prolapse I: Introduction
Mitral Valve Prolapse II: Assessment and Management
Mitral Regurgitation II: Clinical Features and Diagnostic Tests

