Pelvic Lymphovascular Malformation Presenting as a Vulvar Mass in an Adolescent Female

Lymphovascular malformations (LVMs) uncommonly present outside the head and neck region as slow-growing nontender masses. Given their rarity, LVMs are not regularly on the differential for genitopelvic masses. These anomalies are not usually dangerous due to their slow progression and distance from vital structures. Recognition of benign LVMs is important to appropriately counsel regarding treatment options and follow-up.

We describe an occurrence of an extensive pelvic LVM in an adolescent female presenting as a persistent, increasingly uncomfortable growing vulvar mass, highlighting the importance of keeping this diagnosis in mind when dealing with unusual genital masses.

A multidisciplinary approach including consultation with an interventional radiologist and pediatric hematologist is paramount in providing timely care when dealing with a rare diagnosis.