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Updated: Sep 4, 2025
04:44
Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
Published on: June 16, 2020
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Scleroderma and interstitial lung disease - A case report
Fahad Gul1, Amna Siddiqui2, Prakhyath Srikaram3
1Rawalpindi Medical University, Rawalpindi, Pakistan.
Annals of Medicine and Surgery (2012)
|July 18, 2022
Summary
Systemic sclerosis with interstitial lung disease (ILD) is a rare autoimmune disorder. Early detection and management of ILD-SS are crucial to prevent severe complications and mortality.
Area of Science:
- Rheumatology
- Pulmonology
- Autoimmune Diseases
Background:
- Systemic sclerosis (SSc) is an autoimmune disorder with a high mortality rate, often due to associated interstitial lung disease (ILD).
- ILD in SSc patients is a significant cause of morbidity and mortality, underscoring the need for focused research and clinical attention.
Observation:
- A 37-year-old female with known Scleroderma, Cor pulmonale, and hypothyroidism presented with worsening dyspnea and orthopnea.
- Dermatological examination revealed digital gangrene, a known complication of systemic sclerosis.
Findings:
- The patient's presentation of exacerbated dyspnea and orthopnea was linked to pulmonary hypertension secondary to ILD, leading to cor pulmonale.
- Medical management resulted in improvement of the patient's exacerbated symptoms.
Implications:
- This case highlights the critical importance of early diagnosis and proactive management of ILD in systemic sclerosis patients.
- Timely intervention can mitigate disease progression, prevent acute exacerbations, and reduce the overall burden of morbidity and mortality associated with ILD-SS.
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