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Criss cross heart: A challenging diagnosis
Abdul Malik Sheikh1, Asma Kanwal1, Hina Sattar2
1Department of Pediatric Cardiology, Rawalpindi Institute of Cardiology, Rawalpindi, Pakistan.
Insights
Crisscross heart (CCH) is a rare congenital heart defect. Early diagnosis via echocardiography is crucial for improved outcomes in affected children.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Imaging
Background:
- Crisscross heart (CCH) is a rare congenital anomaly.
- Characterized by twisting of ventricular inflow streams.
- Etiology remains largely unknown.
Observation:
- Presents with cyanosis in neonates and shortness of breath in older children.
- A case series of CCH with various associations is presented.
- Echocardiography is the primary diagnostic tool.
Findings:
- CCH is a rare heart defect with a low incidence.
- Diagnosis requires vigilant echocardiographic assessment.
- Associated anomalies can occur in CCH patients.
Implications:
- Early diagnosis of CCH is vital for management.
- Timely intervention improves survival rates.
- Enhanced quality of life is achievable with prompt care.
Abstract:
Crisscross heart (CCH) is a rare anomaly characterized by twisting of the inflow streams of right and left ventricles. The etiology of CCH is not known. Its frequency is less than 8/10, 00,000 live births. Cyanosis is common in neonatal age, while shortness of breath is the main presenting complaint in older children. We present a case series of CCH with array of associations, diagnosed by echocardiography. CCH is a rare heart defect that can be diagnosed by echocardiography by a vigilant operator. Early diagnosis is the key to successful management resulting in increased survival rate, better outcomes and improved quality of life.
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