Extrahepatic Bile Duct Duplication with Intraductal Papillary Neoplasm: A Case Report

Area of Science:

• Gastroenterology and Hepatology
• Surgical Pathology
• Congenital Anomalies

Background:

• Extrahepatic bile duct duplication is an exceptionally rare congenital anomaly.
• Intraductal papillary neoplasm of the bile duct (IPNB) is a rare biliary tumor.
• The co-occurrence of these two conditions has not been previously documented.

Observation:

• A 64-year-old female presented with findings suggestive of a biliary neoplasm.
• Radiologic imaging revealed findings consistent with IPNB in the context of extrahepatic bile duct duplication.
• The patient underwent an extended right hepatectomy for definitive treatment.

Findings:

• Histopathological examination confirmed the presence of intraductal papillary neoplasm of the bile duct (IPNB).
• The findings definitively established the co-existence of IPNB and extrahepatic bile duct duplication in this patient.
• This represents the first reported case of IPNB associated with extrahepatic bile duct duplication.

Implications:

• This case expands the known spectrum of biliary tract pathology.
• Understanding this rare association may influence diagnostic and surgical approaches for similar future cases.
• Further research into the embryological or pathological mechanisms linking these conditions may be warranted.