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Budd-Chiari syndrome in Behçet's disease
Daniel Alvarenga Fernandes1, Carlos Eduardo Garcez Teixeira2, Zoraida Sachetto3
1Radiology, School of Medical Sciences. University of Campinas (UNICAMP), Brazil.
Revista Espanola De Enfermedades Digestivas
|October 20, 2022
Summary
This case study highlights Budd-Chiari Syndrome in Behçet disease, a rare condition presenting with abdominal issues and venous thrombosis. Early diagnosis and immunosuppression led to positive clinical outcomes.
Area of Science:
- Vascular Medicine
- Rheumatology
- Gastroenterology
Background:
- Behçet disease is a multisystemic inflammatory disorder.
- Budd-Chiari Syndrome involves hepatic vein obstruction.
- Co-occurrence of these conditions is rare.
Observation:
- A 36-year-old male presented with abdominal distention, epigastralgia, and weight loss.
- Physical exam revealed abdominal venous collaterals, hepatomegaly, ascites, and edema.
- Endoscopy and imaging showed esophageal varices, ileal ulcer, and extensive venous thrombosis.
Findings:
- Diagnostic workup excluded infection, coagulation, and lymphoproliferative disorders.
- Budd-Chiari Syndrome secondary to Behçet disease was diagnosed.
- Ascitic fluid analysis was non-inflammatory and non-infectious.
Implications:
- This case underscores the importance of considering Behçet disease in young patients with unexplained venous thrombosis.
- Prompt immunosuppressive therapy is crucial for managing Budd-Chiari Syndrome in Behçet disease.
- Multidisciplinary management is essential for optimizing patient outcomes.
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