Left ventricular dysfunction in a child with asymptomatic pre-excitation: Cure with catheter ablation
Nilüfer Çetiner1, Alpay Çeliker2
1Department of Pediatrics, Division of Cardiology, Koç University Faculty of Medicine, İstanbul, Turkey.
Insights
Wolff-Parkinson-White syndrome can cause heart dysfunction in children. Early diagnosis and catheter ablation of accessory pathways can restore normal cardiac function, as seen in a young patient with cryoablation success.
Area of Science:
- Pediatric Cardiology
- Electrophysiology
- Cardiomyopathy Research
Background:
- Wolff-Parkinson-White syndrome (WPW) is associated with left ventricular dysfunction, often secondary to sustained tachycardia in pediatric populations.
- However, ventricular dysfunction directly from pre-excitation's abnormal activation patterns is less commonly reported.
- Early recognition is crucial as intervention can reverse cardiac dysfunction.
Observation:
- A 2.5-year-old patient presented with tachycardia-free WPW syndrome.
- The patient exhibited a right free wall accessory pathway and depressed cardiac function.
- Despite being tachycardia-free, the patient had impaired left ventricular function.
Findings:
- Successful catheter cryoablation was performed to eliminate the accessory pathway.
- Post-ablation, the patient demonstrated complete restoration of left ventricular function.
- This case highlights recovery even without sustained tachycardia.
Implications:
- Catheter ablation of accessory pathways is an effective treatment for WPW-related cardiac dysfunction in children.
- Prompt diagnosis and intervention can lead to rapid and complete recovery of ventricular function.
- This approach offers a potentially life-saving option for pediatric patients with WPW and cardiac compromise.
Abstract:
Wolff-Parkinson-White syndrome, is known to cause left ventricular dysfunction or dilated cardiomyopathy secondary to sustained tachycardia in infants and children. However, left ventricular dysfunction secondary to pre-excitation related abnormal ventricular activation has been reported in a limited number of cases. This condition should be recognized early, as catheter ablation of the accessory pathway can permit rapid ventricular function improvement. In this paper, we present a 2.5-year-old patient diagnosed with tachycardia-free Wolff-Parkinson-White syndrome with a right free wall accessory pathway and depressed cardiac function, whose left ventricular function is completely restored after successful catheter cryoablation.
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