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Curative Pericardiectomy in Interpheron-Resistant Severe Pericardial Erdheim-Chester Disease
Javier Gómez-Herrero1, Carolina Hernández Luis1, Elena Tapia Moral2
1Instituto de Ciencias del Corazón, Cardiology Department, Hospital Clínico Universitario, Valladolid, Valladolid, Spain.
Abstract:
Erdheim-Chester disease is a rare clonal non-Langerhans cell histiocytosis with multisystemic involvement. It affects bones, large vessels, and retroperitoneum. Cardiac involvement is one of the main mortality predictors.1 We present an unusual case that debuted with cardiac tamponade and pericardial constriction requiring pericardiectomy for definitive control. (Level of Difficulty: Intermediate.).
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