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[Westphal-Strumpell disease. Description of a clinical case]
F Nuccetelli1, M Assetta, U Colangelo
1Università degli Studi di Chieti, Clinica Neurologica.
Minerva Medica
|September 15, 1987
Abstract:
A case of hepatolenticular degeneration with the clinical pattern of Westphal-Strumpell disease is described. Diagnosis was based on clinical pattern, absence of hepatic impairment, typical biochemical abnormalities of copper metabolism and response (clinical and biochemical) to D-penicillamine.