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Primary cerebral epithelioid angiosarcoma: a case report
Renzhao Kuang1, Shun Li1, Yuanchuan Wang2
1Department of Neurosurgery, Affiliated Hospital of North Sichuan Medical College, Nanchong, 637000, China.
BMC Neurology
|February 1, 2023
Summary
Primary cerebral epithelioid angiosarcoma (PCEA) is an extremely rare brain tumor. This report details a fourth case, highlighting its aggressive nature and limited survival post-treatment.
Area of Science:
- Neuro-oncology
- Pathology
- Radiology
Background:
- Primary cerebral epithelioid angiosarcoma (PCEA) is a rare central nervous system malignancy.
- Only three cases have been previously documented in English literature.
Observation:
- A 73-year-old male presented with headache, revealing an occipital lobe mass.
- Surgical resection and histopathology confirmed epithelioid angiosarcoma.
- The patient received radiotherapy but experienced recurrence and limited survival.
Findings:
- This case represents the fourth documented instance of PCEA.
- The tumor exhibited aggressive behavior with rapid recurrence.
- Prognosis remains poor despite multimodal treatment.
Implications:
- Adds to the scarce literature on PCEA.
- Underscores the need for further research into PCEA characteristics and treatment.
- Highlights the challenges in managing this rare brain tumor.

