Large isolated major aortopulmonary collateral artery causing dilated left ventricle.

Area of Science:

• Cardiology
• Pediatric Cardiology
• Congenital Heart Disease

Background:

• Isolated major aortopulmonary collateral artery (MAPCA) is a rare congenital anomaly.
• Typically observed in preterm newborns, it often resolves spontaneously with conservative management.
• However, some cases may progress and impact cardiac structure.

Observation:

• A case report of an asymptomatic, full-term 5-month-old infant with a heart murmur.
• Echocardiography showed a dilated left ventricle without pulmonary hypertension.
• Computed tomography angiogram identified a large MAPCA supplying the left lower lobe.

Findings:

• The infant's condition was successfully treated with percutaneous obliteration using Amplatzer vascular plugs.
• This intervention resolved the anomalous connection.
• The infant experienced a positive outcome post-procedure.

Implications:

• While often benign, isolated MAPCA requires monitoring due to potential progression.
• Early intervention, like percutaneous closure, can prevent irreversible cardiac damage.
• This case demonstrates the efficacy of minimally invasive techniques for managing MAPCAs in infants.