[Spinal facioscapulo-peroneal (or facioscapulo-crural) muscular atrophy and facioscapulo-peroneal muscular dystrophy]

A report is presented of a patient with lesions of muscles of the face, shoulder girdle, wrists and shins. The clinical findings were similar to those noted in a patient with facioscapuloperoneal muscular dystrophy. An analysis of statistical and dynamic formulas of muscular lesions with regard to electromyographic findings made it possible to determine the neurogenic nature of the damage. It is shown that under clinical conditions, using the formula of muscular lesions, one may differentiate between facioscapuloperoneal muscular atrophy and facioscapuloperoneal myodystrophy and Stark-Keser's spinal scapuloperoneal atrophy. It is proposed that the term neurogenic "scapulotibial syndrome" should be used instead of "scapuloperoneal" one.