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Anesthetic Considerations for an Adult With Bannayan-Riley-Ruvalcaba Syndrome: A Case Report.
Catherine M Pivalizza1, Hayden B Jefferies, Evan G Pivalizza
1From the Department of Anesthesiology, McGovern Medical School, UTHouston, Houston, Texas.
A&A Practice
|July 6, 2023
Summary
Anesthetic management for Bannayan-Riley-Ruvalcaba syndrome presents challenges due to potential airway issues. High-flow nasal oxygen and videolaryngoscopy successfully secured the airway in a patient with difficult anatomy.
Area of Science:
- Anesthesiology
- Genetics
- Pediatric Surgery
Background:
- Bannayan-Riley-Ruvalcaba syndrome (BRRS) is a rare genetic disorder associated with PTEN hamartoma tumor syndrome.
- Patients with BRRS may require surgery for various associated conditions, including tumors and malformations.
- Anesthetic implications for BRRS, particularly airway management, are not well-documented.
Observation:
- Airway management in BRRS can be difficult due to macrocephaly and lymphangiomatous tissue.
- Developmental delay in affected individuals may preclude awake airway management techniques.
Findings:
- This report details the anesthetic management of a BRRS patient with challenging airway anatomy.
- Successful airway secured using high-flow nasal oxygen and videolaryngoscopy.
Implications:
- Highlights the need for specialized anesthetic protocols for BRRS patients.
- Emphasizes the utility of videolaryngoscopy in managing difficult airways in BRRS.
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